Fig. 1

Clinical course of the patient with FIC1 deficiency (case 1). FIC1 progressive familial intrahepatic cholestasis 1, ALT alanine aminotransferase, D-Bil direct bilirubin, CHDF continuous hemodiafiltration, PEBD partial external biliary diversion, LDLT living-donor liver transplantation, TEBD total external biliary diversion