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Table 2 Literature review of liver transplantation for the cases with Turner syndrome

From: Liver transplantation for a patient with Turner syndrome presenting severe portal hypertension: a case report and literature review

Case no.

Age at LT

Indication of LT

Type of LT

Histology of explanted liver

Outcome

Ref. no.

1

n/d

Uncontrolledvaricealbleeding, intractable cholestasis

OLT

Obliterative portal venopathy, periductal fibrosis, multiple focal nodular hyperplasia

n/d

7

2

52 years

Encephalopathy, gastrointestinal bleeding, refractory ascites/hydrothorax, hepatorenal syndrome

OLT

Atrophic liver, portal vein aneurysm and thrombus, small portal branches, no fibrosis

Died

8

3

44 years

Worsening liver function

OLT?

n/d

Alive

9

Current case

30 years

Variceal bleeding, refractory ascites, hypersplenism

LDLT

Obliterative portal venopathy, sinusoidal dilatation

Alive

  1. LDLT living donor liver transplantation, n/d not described, OLT orthotopic liver transplantation