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Table 1 Clinical factors of the current case and 35 reviewed cases of EACC reported in Japan from 1990 to 2014

From: A case of adenoid cystic carcinoma of the esophagus

Year

Age/sex

Endoscopic appearance

Biopsy

Treatment

Depth of invasion

Lymph node metastasis

Lymphatic invasion

Vascular invasion

Observation period (month)

Outcome (cause of death)

Present

78/M

Protruding

ACC

Surgery

SM

2

Alive

1995

74/M

Elevated

ACC

Surgery

SM

+

+

12

Alive

1991

70/M

Protruding

ACC

Surgery

SM

+

N.A

N.A

1995

59/M

Protruding

ACC

Surgery

SM

13

Alive

2011

67/F

Protruding

ACC

Surgery

SM

N.A

N.A

2012

64/M

Protruding

ACC

Surgery

SM

N.A

N.A

2005

81/M

N.A

N.A

Surgery

SM

N.A

N.A

69

Dead (other disease)

2005

69//M

N.A

N.A

Surgery

SM

N.A

N.A

51

Alive

1997

53/M

Elevated

SCC

Surgery

SM

+

+

36

Alive

1994

81/M

Ulcerative

SCC

Surgery

SM

26

Alive

2001

71/M

Protruding

SCC

Surgery

SM

41

Alive

2010

60/M

Protruding

SCC

NAC + surgery

SM

5

Alive

1997

81/M

N.A

N.A

Surgery

SM

22

Alive

2003

65/M

Protruding

N.A

Surgery

SM

+

4

Dead (other disease)

1990

74/M

Protruding

SCC

Surgery

SM

30

Alive

1992

70/F

Protruding

N.A

Surgery

SM

142

Alive

1990

69/M

Protruding

SCC

Surgery

SM

6

Alive

1990

73/M

Protruding

SCC

Surgery

SM

18

Alive

1998

48/F

Ulcerative

ACC

Surgery

MP

+

+

+

36

Alive

1996

57/M

N.A

N.A

Chemotherapy + surgery

MP

+

+

56

Alive

2005

68/M

N.A

N.A

Surgery

MP

N.A

N.A

2

Alive

1994

59/M

Elevated

SCC

Surgery

MP

+

60

Alive

1991

64/M

Ulcerative

SCC

Surgery

MP

11

Alive

1992

59/M

Ulcerative

SCC

Surgery

MP

+

42

Alive

1996

79/M

Protruding

Adeno

Surgery

MP

N.A

N.A

30

Alive

1994

61/M

Ulcerative

ACC

Surgery

AD

N.A

+

12

Dead (EACC)

2007

51/M

Ulcerative

ACC

Surgery

AD

+

2

Alive

1994

71/M

Protruding

ACC

Surgery

AD

+

+

+

5

Dead (other disease)

2005

41/M

N.A

N.A

Radiation

AD

-

N.A

N.A

22

Dead (EACC)

1991

57/M

Elevated

SCC

Surgery

AD

+

N.A

N.A

N.A

N.A

1996

68/F

Protruding

SCC

Surgery

AD

N.A

N.A

N.A

N.A

1992

64/M

Elevated

N.A

Surgery

AD

+

+

15

Dead (EACC)

1993

77/F

Protruding

ACC

Chemotherapy

AI (aorta)

+

N.A

N.A

9

Dead (EACC)

1992

55/M

Ulcerative

SCC

Surgery

AI (trachea)

+

+

+

7

Dead (EACC)

2005

84/M

N.A

N.A

Surgery

AI

+

N.A

N.A

40

Alive

1997

70/F

Protruding

SCC

Surgery

N.A

+

N.A

N.A

30

Dead (other disease)

  1. N.A not available, adeno adenocarcinoma, NAC neoadjuvant therapy, SM submucosa, MP muscle, AD adventitia, AI invasion to adjacent organ