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Table 1 Reported cases of primary pancreatic leiomyosarcoma in the English literature

From: Primary leiomyosarcoma of the pancreas: report of a case treated by local excision and review of the literature

Case

Author

Year

Age, year/sex

Site/size, cm

Distant metastasis

Treatment

Grade

IHC

Outcome/follow up, months

1

Ross [5]

1951

80/M

Whole pancreas

Widespread

Autopsy case

High

n.a.

DOD

2

Berman and Levene [6]

1956

47/M

Head/5.5

No

PD

n.a.

n.a.

ANED/12

3

Feinberg et al [7]

1957

14/M

Head/11.0

No

PD

Low

n.a.

n.a.

4–8

Baylor and Berg (n = 5) [4]

1973

51 (median)/3M, 2F

Body-tail/n.a.

1 localised, 1 locally advanced, 3 disseminated

n.a.

n.a.

n.a.

ANED (n = 1)/1; DOD (n = 3)/14 (median)

9

Ishikawa et al [8]

1981

44/M

Head/8.0

No

PD/CT

Low

n.a.

DOD/48

10

Lakhoo and Mannell [9]

1991

68/M

Body/17.0

No

DP, gastric resection, transverse colectomy

Low

n.a.

ANED/24

11

de Alava et al [10]

1993

71/M

Body/3.6

No

DP

n.a.

(+) desmin, smooth muscle actin, vimentin; (−) AE1/AE3, CAM5.2

n.a.

12

Peskova and Fried [11]

1994

68/F

Head/15.0

No

PD

Low

n.a.

ANED/36

13

Sato et al [12]

1994

53/F

Body/25.0

No

DP

n.a.

(+) desmin, smooth muscle actin; (−) S-100, EMA

n.a.

14

Ishii et al [13]

1994

66/M

Tail/4.5

Liver

Non resectable/CT

n.a.

(+) desmin, smooth muscle actin

DOD/33

15

Aranha et al [14]

1995

46/F

Body/3.0

No

DP/CT

High

(+) desmin; (−) S-100, cytokeratin, HMB-45

DOD/9

16

Owen et al [15]

1997

40/M

Head/7.0

No

PD

n.a.

(+) desmin, smooth muscle actin

ANED/120

17

Shimizu et al [16]

1997

49/F

Head/15.0

Lung

Non resectable/CT

n.a.

(+) desmin, smooth muscle actin; (−) S-100

DOD/3

18

Chawla et al [17]

1998

45/F

Head/9.2

Lung

Non resectable/CT

Low

(+) smooth muscle actin

AWD/19

19

Paciorek and Ross [18]

1998

63/F

Body/2.0

Mesentery, single

DP

n.a.

n.a.

ANED/n.a.

20

Zalatnai et al [19]

1998

57/M

Head/6.0

Liver

Non resectable

3

(+) smooth muscle actin, SMA; (−) S-100, desmin

DOD/7

21

Ferlan-Marolt et al [20]

2000

57/F

Body-tail/12.0

No

DP

2

(+) SMA; (−) desmin

DOC/p.o. period

22

Machado et al [21]

2000

52/M

Head/7.5

No

PD

Low

(+) SMA; (−) S-100

ANED/24

23

Deveaux et al [22]

2001

44/F

Head/5.0

No

PD

1

(+focal) smooth muscle actin; (−) S-100, keratin

ANED/48

24

Nesi et al [23]

2001

76/M

Tail/8.0

No

DP

High

(+) smooth muscle actin, SMA; (−) desmin, CD34, cytokeratin, S-100

DOD/12

25

Aihara et al [24]

2002

25/F

Body/3.5

No

Local excision

n.a.

(+) desmin, smooth muscle actin; (−) S-100

ANED/42

26

Komoda et al [25]

2002

52/F

Head/1.5

No

PD

Low

(+) desmin, smooth muscle actin; (−) S-100, CD34, KIT

ANED/12

27

Maarouf et al [26]

2007

40/F

Tail/5.0

No

DP

Low

(+) desmin, smooth muscle actin, H-caldesmon; (−) CD34

ANED/240

28

Muhammad et al [27]

2008

73/M

Body/10.0

Liver

Non resectable/CT

Low to intermediate

(+) desmin, smooth muscle actin; (−) S-100, CD34, cytokeratin AE1/AE3, HMB45

DOD/3

29-37

Zhang H et al [28] (n = 9)

2010

63 (median)/5M, 4F

Head (n = 7); Tail (n = 2)/8.0 (median)

Liver (n = 4)

PD (n = 4); Palliative/biopsy (n = 5)

Grades 4 (n = 1), 3 (n = 5), 2 (n = 3)

(+) smooth muscle actin, desmin; (−) KIT

DOD (n = 5), DOC/Unknown (n = 4)/13 (median)

38

Riddle et al [29]

2010

83/F

Tail/8.2

No

DP

2

(+) smooth muscle actin, desmin, vimentin; (−) c-kit, CD34, S-100, pan-cytokeratin

ANED/8

39

Zhang et al [30]

2011

56/F

Body-tail/13.0

No

DP

2

(+) desmin, smooth muscle actin, H-caldesmon, vimentin; (−) cytokeratin, CD34, S-100, CD117

ANED/14

40

Hur et al [31]

2011

70/F

Head/5.0

No

PD

2

(+) actin, vimentin, desmin; (−) cytokeratin, S-100, CD34, CD117

DOD/22

41

Izumi et al [32]

2011

41/F

Body/4.5

No

DP

n.a.

(+) smooth muscle actin, desmin, vimentin

ANED/14

42

Vanderpuye et al [33]

2011

59/F

Tail/24.0

Liver, transverse colon

DP/ CT + RT

n.a.

n.a.

AWD/24

43

Moletta et al [34]

2012

54/F

Body and tail/13.0

Liver

DP, left hepatectomy/CT

3

(+) smooth muscle actin, desmin; (−) cytokeratin, CD34, S-100, CD117

AWD/37

44

Kim et al [3]

2014

51/F

Tail/5.5

No

DP/RT

2

(+) desmin, SMA; (−) CD117, HMB45, CD34

ANED/27

45

Present case

2014

60/F

Head/10.0

No

Local excision

2

(+) smooth muscle actin, desmin, caldesmon;(−) S-100, CD117

ANED/19

  1. ANED alive and no evidence of disease, AWD alive with disease, cm centimetres, CT chemotherapy, DOC died of other cause, DOD died of disease, DP distal pancreatectomy, IHC immunohistochemistry, n number of cases, n.a. not available, PD pancreatico-duodenectomy, p.o. postoperative, RT radiotherapy