Case | Author | Year | Age, year/sex | Site/size, cm | Distant metastasis | Treatment | Grade | IHC | Outcome/follow up, months |
---|---|---|---|---|---|---|---|---|---|
1 | Ross [5] | 1951 | 80/M | Whole pancreas | Widespread | Autopsy case | High | n.a. | DOD |
2 | Berman and Levene [6] | 1956 | 47/M | Head/5.5 | No | PD | n.a. | n.a. | ANED/12 |
3 | Feinberg et al [7] | 1957 | 14/M | Head/11.0 | No | PD | Low | n.a. | n.a. |
4–8 | Baylor and Berg (n = 5) [4] | 1973 | 51 (median)/3M, 2F | Body-tail/n.a. | 1 localised, 1 locally advanced, 3 disseminated | n.a. | n.a. | n.a. | ANED (n = 1)/1; DOD (n = 3)/14 (median) |
9 | Ishikawa et al [8] | 1981 | 44/M | Head/8.0 | No | PD/CT | Low | n.a. | DOD/48 |
10 | Lakhoo and Mannell [9] | 1991 | 68/M | Body/17.0 | No | DP, gastric resection, transverse colectomy | Low | n.a. | ANED/24 |
11 | de Alava et al [10] | 1993 | 71/M | Body/3.6 | No | DP | n.a. | (+) desmin, smooth muscle actin, vimentin; (−) AE1/AE3, CAM5.2 | n.a. |
12 | Peskova and Fried [11] | 1994 | 68/F | Head/15.0 | No | PD | Low | n.a. | ANED/36 |
13 | Sato et al [12] | 1994 | 53/F | Body/25.0 | No | DP | n.a. | (+) desmin, smooth muscle actin; (−) S-100, EMA | n.a. |
14 | Ishii et al [13] | 1994 | 66/M | Tail/4.5 | Liver | Non resectable/CT | n.a. | (+) desmin, smooth muscle actin | DOD/33 |
15 | Aranha et al [14] | 1995 | 46/F | Body/3.0 | No | DP/CT | High | (+) desmin; (−) S-100, cytokeratin, HMB-45 | DOD/9 |
16 | Owen et al [15] | 1997 | 40/M | Head/7.0 | No | PD | n.a. | (+) desmin, smooth muscle actin | ANED/120 |
17 | Shimizu et al [16] | 1997 | 49/F | Head/15.0 | Lung | Non resectable/CT | n.a. | (+) desmin, smooth muscle actin; (−) S-100 | DOD/3 |
18 | Chawla et al [17] | 1998 | 45/F | Head/9.2 | Lung | Non resectable/CT | Low | (+) smooth muscle actin | AWD/19 |
19 | Paciorek and Ross [18] | 1998 | 63/F | Body/2.0 | Mesentery, single | DP | n.a. | n.a. | ANED/n.a. |
20 | Zalatnai et al [19] | 1998 | 57/M | Head/6.0 | Liver | Non resectable | 3 | (+) smooth muscle actin, SMA; (−) S-100, desmin | DOD/7 |
21 | Ferlan-Marolt et al [20] | 2000 | 57/F | Body-tail/12.0 | No | DP | 2 | (+) SMA; (−) desmin | DOC/p.o. period |
22 | Machado et al [21] | 2000 | 52/M | Head/7.5 | No | PD | Low | (+) SMA; (−) S-100 | ANED/24 |
23 | Deveaux et al [22] | 2001 | 44/F | Head/5.0 | No | PD | 1 | (+focal) smooth muscle actin; (−) S-100, keratin | ANED/48 |
24 | Nesi et al [23] | 2001 | 76/M | Tail/8.0 | No | DP | High | (+) smooth muscle actin, SMA; (−) desmin, CD34, cytokeratin, S-100 | DOD/12 |
25 | Aihara et al [24] | 2002 | 25/F | Body/3.5 | No | Local excision | n.a. | (+) desmin, smooth muscle actin; (−) S-100 | ANED/42 |
26 | Komoda et al [25] | 2002 | 52/F | Head/1.5 | No | PD | Low | (+) desmin, smooth muscle actin; (−) S-100, CD34, KIT | ANED/12 |
27 | Maarouf et al [26] | 2007 | 40/F | Tail/5.0 | No | DP | Low | (+) desmin, smooth muscle actin, H-caldesmon; (−) CD34 | ANED/240 |
28 | Muhammad et al [27] | 2008 | 73/M | Body/10.0 | Liver | Non resectable/CT | Low to intermediate | (+) desmin, smooth muscle actin; (−) S-100, CD34, cytokeratin AE1/AE3, HMB45 | DOD/3 |
29-37 | Zhang H et al [28] (n = 9) | 2010 | 63 (median)/5M, 4F | Head (n = 7); Tail (n = 2)/8.0 (median) | Liver (n = 4) | PD (n = 4); Palliative/biopsy (n = 5) | Grades 4 (n = 1), 3 (n = 5), 2 (n = 3) | (+) smooth muscle actin, desmin; (−) KIT | DOD (n = 5), DOC/Unknown (n = 4)/13 (median) |
38 | Riddle et al [29] | 2010 | 83/F | Tail/8.2 | No | DP | 2 | (+) smooth muscle actin, desmin, vimentin; (−) c-kit, CD34, S-100, pan-cytokeratin | ANED/8 |
39 | Zhang et al [30] | 2011 | 56/F | Body-tail/13.0 | No | DP | 2 | (+) desmin, smooth muscle actin, H-caldesmon, vimentin; (−) cytokeratin, CD34, S-100, CD117 | ANED/14 |
40 | Hur et al [31] | 2011 | 70/F | Head/5.0 | No | PD | 2 | (+) actin, vimentin, desmin; (−) cytokeratin, S-100, CD34, CD117 | DOD/22 |
41 | Izumi et al [32] | 2011 | 41/F | Body/4.5 | No | DP | n.a. | (+) smooth muscle actin, desmin, vimentin | ANED/14 |
42 | Vanderpuye et al [33] | 2011 | 59/F | Tail/24.0 | Liver, transverse colon | DP/ CT + RT | n.a. | n.a. | AWD/24 |
43 | Moletta et al [34] | 2012 | 54/F | Body and tail/13.0 | Liver | DP, left hepatectomy/CT | 3 | (+) smooth muscle actin, desmin; (−) cytokeratin, CD34, S-100, CD117 | AWD/37 |
44 | Kim et al [3] | 2014 | 51/F | Tail/5.5 | No | DP/RT | 2 | (+) desmin, SMA; (−) CD117, HMB45, CD34 | ANED/27 |
45 | Present case | 2014 | 60/F | Head/10.0 | No | Local excision | 2 | (+) smooth muscle actin, desmin, caldesmon;(−) S-100, CD117 | ANED/19 |